Bilateral giant renal angiomyolipoma associated with hepatic lipoma in a patient with tuberous sclerosis

  • Edison Daniel Schneider-Monteiro University of São Paulo; Faculty of Medicine; Hospital das Clínicas; Surgery Department
  • Antonio Marmo Lucon University of São Paulo; Faculty of Medicine; Hospital das Clínicas; Surgery Department
  • André Avarese de Figueiredo University of São Paulo; Faculty of Medicine; Hospital das Clínicas; Surgery Department
  • Aldo Junqueira Rodrigues Junior University of São Paulo; Faculty of Medicine; Hospital das Clínicas; Surgery Department
  • Sami Arap University of São Paulo; Faculty of Medicine; Hospital das Clínicas; Surgery Department
Keywords: Angiomyolipoma, Tuberous sclerosis, Hepatic lipoma, Nephron-sparing surgery, Therapeutic

Abstract

OBJECTIVE: To report a case of bilateral giant renal angiomyolipoma associated with tuberous sclerosis, with successful treatment, and to review the literature concerning angiomyolipoma treatment. CASE REPORT: Patient with tuberous sclerosis and angiomyolipoma diagnosed by ultrasonography during her pregnancy. At that time, the angiomyolipoma on the right side was 9 cm in diameter. Conservative management was selected during her pregnancy. The patient returned 7 years later, with a 24.7 x 19.2 x 10.7 cm tumor on the right side and another of 13 x 11.5 x 6.5 cm on the left side, in addition to multiple small angiomyolipomas. A nephron-sparing surgery with tumoral enucleation was performed on the right side, and after 3 months, the tumor on the left side was removed. Renal function in the post-operative period was preserved, and contrast medium progression was uniform and adequate in both kidneys. CONCLUSION: We conclude that an angiomyolipoma larger than 4 cm should be removed surgically, since they have a greater growth rate and pose a risk of hemorrhage. Resection of smaller tumors is safe and has decreased morbidity. Tumoral enucleation is an effective treatment method that preserves kidney function.
Published
2003-01-01
How to Cite
Schneider-Monteiro, E., Lucon, A., Figueiredo, A., Rodrigues Junior, A., & Arap, S. (2003). Bilateral giant renal angiomyolipoma associated with hepatic lipoma in a patient with tuberous sclerosis . Revista Do Hospital Das Clínicas, 58(2), 103-108. https://doi.org/10.1590/S0041-87812003000200008
Section
Case Reports