Knee and ankle disorders during functional gait in mucopolysaccharidosis type VI

Bárbara Bernardo  Figueirêdo; Paulo  Magalhães; Breno  Azevedo; Maria Lucila  Cavalcanti; Maria Emília  Melo; Cinthia  Vasconcelos

doi:10.1590/1809-2950/21003228012021

Authors

Bárbara Bernardo Figueirêdo Universidade Federal de Pernambuco (UFPE) - Recife (PE), Brasil http://orcid.org/0000-0002-4949-6268
Paulo Magalhães Universidade Federal de Pernambuco (UFPE) - Recife (PE), Brasil http://orcid.org/0000-0002-2224-9291
Breno Azevedo Universidade Federal de Pernambuco (UFPE) - Recife (PE), Brasil http://orcid.org/0000-0003-4917-8726
Maria Lucila Cavalcanti Universidade Federal de Pernambuco (UFPE) - Recife (PE), Brasil http://orcid.org/0000-0001-9957-6656
Maria Emília Melo Universidade Federal de Pernambuco (UFPE) - Recife (PE), Brasil http://orcid.org/0000-0001-9924-0466
Cinthia Vasconcelos Universidade Federal de Pernambuco (UFPE) - Recife (PE), Brasil http://orcid.org/0000-0003-0604-7697

DOI:

https://doi.org/10.1590/1809-2950/21003228012021

Keywords:

Mucopolysaccharidosis VI, Gait, Range of Motion, Articular

Abstract

To evaluate knee and ankle disorders during functional gait assessment in individuals with Mucopolysaccharidosis type VI (MPS VI). 19 subjects were included in this cross-sectional study and allocated in three groups according to age: Children Group (n=11); Adolescent Group (n=4); and Adult Group (n=4). Subphases of one gait cycle were analyzed: Initial contact; Medium support, and Pre-Balance. All volunteers with MPS VI presented greater knee and ankle flexion angles, in all gait subphases, when compared to the normal values defined by literature (p<0.05). Initial contact subphase: knee flexion angle ranging from 8.5º to 15º; Ankle = Child Group −23.73º ± 8.53º; Adolescent Group = −25º ± 11.22º; Adult Group = 27.75º ± 3.3º. Medium support subphase: Knee = Child Group 19.64º± 10.47º; Adolescent Group 16.75º ± 10.34º; Adult Group = 21.25º ± 12.84º.Ankle = Child Group −18.82º ± 8.91º ± 8.53º; Adolescent Group = −16.5º ± 9.33º; Adult Group = −22.25º± 4.19º. Pre-Balance subphase: Knee = Child Group 22.72º ± 13.49º; Adolescent Group 21.25º ± 7.97º; Adult Group = 27º ± 16.27º. Ankle = Child Group -15º ± 9.76º; Adolescent Group = −15.75º ± 5.31º; Adult Group = −14.75º ± 3.86º. In this study, MPS VI individuals presented hyperflexion of knee and ankle as the main joint disorders during functional gait, regardless of age.

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Knee and ankle disorders during functional gait in mucopolysaccharidosis type VI

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