IgA vasculitis in a child: case report
DOI:
https://doi.org/10.11606/issn.1679-9836.v101i5e-195839Keywords:
Children, Henoch Schonlein Purpura, Small Vessel Vasculitis, IgA VasculitesAbstract
Vasculitis associated with immunoglobulin A (VIgA), also known as Henoch-Schonlein purpura, anaphylactoid purpura or rheumatic purpura is a small vessel vasculitis associated with deposition of IgA immune complexes, of unknown etiology and affecting mainly children. In most pediatric cases, it is a self-limited disease with cutaneous, joint, gastrointestinal and renal manifestations. The differential diagnosis includes other vasculitis, such as systemic lupus erythematosus, meningococcemia, disseminated intravascular coagulation and uremic hemolytic syndrome. In this article, the main aspects of HSP in children are addressed, highlighting the importance of early differential diagnosis. The clinical case of a 5-year-old female patient with purpuric lesions treated in a first approach as a severe bacterial infection is presented. After medical re-evaluation, there was a therapeutic change with the use of glucocorticoids resulting in a significant improvement of symptoms.
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Copyright (c) 2022 Ana Beatriz Montans Sallum, Eduarda Guedes Narciso , Magda Regina Silva Moura, Marco Antônio Sallum
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